ABSTRACT
Most developmental abnormalities are manifest at birth but others present with delayed puberty, sexual problems, infertility or obstructed labor. The cause of developmental abnormalities is usually not known, but they are occasionally familial and some may be associated with renal, lower gastro-intestinal tract and distant maldevelopments. Duplication of the vulva is an extremely rare genital malformation often associated with other multiple organ abnormalities that are incompatible with survival. A developmental cyst due to embryological inclusion during ectodermal fusion is known as a dermoid cyst. Such developmental cysts, found along developmental fusion fines, particularly on the face, are occasionally found in the vulva. Vascular dilatations are seen in hereditary hemorrhagic telangiectasia (Osier’s disease), spider angiomas and angiokeratomas. An ectopic ureter may be the sole drainage from a kidney, part of a duplex system, unilateral or bilateral. It may open into the urinary system distal to the trigone or into the vagina.
