ABSTRACT
This chapter reviews the pathogenesis and diagnosis of the rare malformation, and discusses its implication on the management of infertile female. It focuses on ectopic locations above the pelvic brim. In patients with unicornuate uterus, the undescended ovary and fallopian tube occurred on the contralateral side. The higher incidence of ovarian maldescent in patients with unicornuate uterus, bicornuate uterus, uterus didelphys, and Mullerian agenesis can be explained on the basis that all such anomalies occur during Mullerian duct migration and uterine body fusion. Renal anomalies were found in 23%–24.6% patients with Mullerian anomalies and 36% in patients with both Mullerian anomalies and ovarian maldescent. However, if the patient presents with pain, continuous treatment with oral contraceptives may be indicated, especially in the presence of recurrent ovarian cysts or associated endometriosis. Conservative treatment of associated endometriosis at time of laparoscopy should be attempted in patients with maldescent ovaries and pain and/or infertility.
